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Image of a neural disease that would cause high-frequency hearing loss.

Do you spend much time thinking about your nervous system? For most individuals, the answer would most likely be not very frequently. As long as your body is working as it should, you have no reason to consider how your neurons are firing or whether nerves are sending correct messages along the electrical pathways in your body. But when those nerves start to misfire – that is when something fails – you tend to pay a lot more attention to your nervous system.

One distinct disease called Charot-Marie-Tooth Disease which normally affects the extremities can also have a pretty wide-scale impact on the overall nervous system. And there’s some evidence to suggest that CMT can also lead to high-frequency hearing loss.

Charot-Marie-Tooth Disease, What is it?

Charcot-Marie-Tooth disease is a set of inherited conditions. In essence, these genetic disorders cause something to go wrong with your nerves or with the protective sheathing around your nerves.

There is a problem with how impulses travel between your brain and your nerves. Functionally, this can result in both a loss in motor function and a loss of feeling.

A mix of genetic elements typically leads to the manifestation of symptoms, so CMT can be present in a number of variations. Symptoms of CMT commonly begin in the feet and work their way up to the arms. And, strangely, among those who have CMT, there is a higher rate of occurrence of high-frequency hearing loss.

A Connection Between Loss of Hearing And CMT: The Cochlear Nerve

The connection between CMT and hearing loss has always been colloquially recognized (that is, everybody knows someone who has a tells about it – at least within the CMT community). And it seemed to confuse people who had CMT – the ear didn’t seem very related to the loss of sensation in the legs, for example.

The connection was firmly established by a scientific study just recently when a group of researchers evaluated 79 people with CMT at the University of Iowa Hospitals and Clinics.

The results were quite conclusive. Low to moderate frequencies were heard nearly perfectly by those with CMT. But high-frequency sounds (in the moderate region in particular) were effortlessly heard by all of the participants. high-frequency hearing loss, according to this research, is likely to be linked to CMT.

What is The Cause of Hearing Loss And How Can it be Addressed?

At first, it might be perplexing to attempt to figure out the link between high-frequency hearing loss and CMT. But everything in your body, from your toes to your eyebrows, relies on the correct functioning of nerves. That’s also the same for your ears.

What most researchers hypothesize occurs is that the cochlear nerve is impacted by the CMT – disrupting your ear’s ability to translate and transmit sounds in a high-frequency range. Anyone with this form of hearing loss will have difficulty hearing specific sounds, including peoples voices. Trying to understand voices in a crowded noisy room is particularly difficult.

This type of hearing loss is normally treated with hearing aids. There’s no recognized cure for CMT. Modern hearing aids can provide considerable help in terms of fighting the effects of high-frequency loss of hearing, selecting only those ranges of sounds to amplify. In addition, most modern hearing aids can be adjusted to function well inside of noisy settings.

There Can be Various Causes For Hearing Loss

Further than the unconfirmed hypothesis, it’s still not well understood what the relationship between high-frequency hearing loss and CMT is. But this kind of hearing loss can be effectively treated using hearing aids. So scheduling an appointment to get fitted for hearing aids will be a good decision for individuals who suffer from CMT.

Hearing loss symptoms can develop for many reasons. Commonly, it’s a matter of loud noise contributing to damage to the ears. Obstructions can be another cause. It also looks as if CMT is another possible cause.

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